Inherited anomalies of bones and joints of the hands.
In 1965, Z. Banki, a Hungarian
physician, described the syndrome in three generations of the same Hungarian
family. Assumed to be a unique, autosomal dominant inherited mutation.
Family members affected with the syndrome
demonstrate fusion of the cuneiform and lunate bones of the wrist,
clinometacarpia, brachymetacarpia, leptometacarpia, and clinodactyly. No
other systemic manifestations of this condition occurred.
Care with positioning of the wrists
during anesthesia because of decreased mobility and increased susceptibility
of the wrist joints to trauma. Venous access may be difficult in hands.
Banki Z: Kombination erblicher Gelenk-und Knochenanomalien an der Hand.
Zwei neue Röntgenzeichen. Fortschr Röntgenstr 103:598, 1965.